Treatment of rapidly progressive systemic sclerosis: current and futures perspectives
نویسندگان
چکیده
منابع مشابه
Progressive systemic sclerosis.
The pulmonary manifestations of progressive systemic sclerosis (PSS) are important determinants of a patient’s prognosis. Although the etiology and pathogenesis of PSS are unknown, it is recognized that this is a complex disease; it is likely that different genetic susceptibilities and environmental exposures lead to the disease in different individuals. Individuals with diffuse PSS tend to dev...
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Systemic sclerosis (SSc or scleroderma) is a progressive and highly debilitating autoimmune disorder characterized by inflammation, vasculopathy, and extensive fibrosis. SSc is highly heterogeneous in its clinical presentation, extent and severity of skin and internal organ involvement, and clinical course and has the highest fatality rate among connective tissue diseases. While clinical outcom...
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In this report, we describe the use of extracorporeal photochemotherapy in n the treatment of two patients with rapidly advancing progressive systemic sclerosis. Both patients experienced improvement in the cutaneous as well as the systemic manifestations of their disease while undergoing therapy. The potential therapeutic mechanisms are discussed.
متن کاملradiological findings in progressive systemic sclerosis (p.s.s.)
radiological findings of 20 patients with scleroderma have been described. we had cornmon and uncommon roentgen signs of scleroderma similar to other series and one case with mid esophagus narrowing which we think have not been reported previously.
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ژورنال
عنوان ژورنال: Expert Opinion on Orphan Drugs
سال: 2015
ISSN: 2167-8707
DOI: 10.1517/21678707.2016.1114454